Felipe Terpin-Ayvar, Facultad de Medicina Alberto Hurtado, Universidad Peruana Cayetano Heredia, Lima, Perú
Fanny Otiniano-Costa, Servicio de Cardiología, Departamento de Medicina, Hospital Nacional Cayetano Heredia, Lima, Perú
Aida Rotta-Rotta, Servicio de Cardiología, Departamento de Medicina, Hospital Nacional Cayetano Heredia, Lima, Perú
Luis S. Velarde Zegarra, Facultad de Medicina San Fernando, Universidad Nacional Mayor San Marcos, Lima, Perú
The case of a 45-year-old woman with tetralogy of Fallot associated with complete atrioventricular block is presented. The patient presented with episodes of recurrent syncope, progressive dyspnea (NYHA II) and chronic precordial pain. After diagnosis, a permanent pacemaker was implanted, achieving clinical stabilization and dyspnea improvement (NYHA II to I). This case highlights the importance of timely diagnosis and multidisciplinary management in adults with untreated congenital heart disease, emphasizing the role of early interventions in improving quality of life and survival.
Keywords: Tetralogy of Fallot. Congenital heart disease. Atrioventricular block. Pacemaker. Echocardiography.